α-L-Iduronidase is an essential lysosomal enzyme responsible for the degradation of glycosaminoglycans (GAGs) such as dermatan sulfate and heparan sulfate. It plays a crucial role in the breakdown and recycling of complex carbohydrates within the lysosomes. The enzyme specifically catalyzes the hydrolysis of terminal α-L-iduronic acid residues in GAGs, facilitating their subsequent degradation.
